Imperial College London

Professor Konstantinos Dimopoulos

Faculty of MedicineNational Heart & Lung Institute

Professor of Practice (Adult Congenital Heart Disease)
 
 
 
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Contact

 

+44 (0)20 7352 8121 ext 82771k.dimopoulos02

 
 
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Location

 

Chelsea WingRoyal Brompton Campus

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Summary

 

Publications

Citation

BibTex format

@article{Favoccia:2019:10.1080/14779072.2019.1623024,
author = {Favoccia, C and Constantine, AH and Wort, SJ and Dimopoulos, K},
doi = {10.1080/14779072.2019.1623024},
journal = {Expert Review of Cardiovascular Therapy},
pages = {449--459},
title = {Eisenmenger syndrome and other types of pulmonary arterial hypertension related to adult congenital heart disease},
url = {http://dx.doi.org/10.1080/14779072.2019.1623024},
volume = {17},
year = {2019}
}

RIS format (EndNote, RefMan)

TY  - JOUR
AB - Introduction: Eisenmenger syndrome (ES) is the most advanced form of pulmonary arterial hypertension (PAH) in patients with congenital heart disease (CHD). It is characterised by a severe rise in pulmonary vascular resistance resulting in shunt reversal and cyanosis. Areas covered: In this paper, an overview of ES and other types of PAH related to CHD (PAH-CHD) in adults is provided. The modern management of PAH-CHD in tertiary centers, with emphasis on co-morbidities and complications is described. Expert opinion: PAH-CHD is a wide spectrum of conditions, of which ES is the archetype. The size and location of the shunt, the degree of adaptation of the right ventricle to the increased afterload and other compensatory mechanisms, such as secondary erythrocytosis, define the clinical presentation and natural history of these patients. PAH therapies have improved the quality of life and outcome of many patients with PAH-CHD, but expert multidisciplinary management remains essential in optimising the care of this rare and complex group of patients.
AU - Favoccia,C
AU - Constantine,AH
AU - Wort,SJ
AU - Dimopoulos,K
DO - 10.1080/14779072.2019.1623024
EP - 459
PY - 2019///
SN - 1477-9072
SP - 449
TI - Eisenmenger syndrome and other types of pulmonary arterial hypertension related to adult congenital heart disease
T2 - Expert Review of Cardiovascular Therapy
UR - http://dx.doi.org/10.1080/14779072.2019.1623024
UR - https://www.ncbi.nlm.nih.gov/pubmed/31120797
UR - http://hdl.handle.net/10044/1/70517
VL - 17
ER -