Imperial College London

DrSonyaBabu-Narayan

Faculty of MedicineNational Heart & Lung Institute

Reader in Adult Congenital Heart Disease
 
 
 
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Contact

 

+44 (0)20 7351 8803s.babu-narayan

 
 
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Location

 

NIHR Cardiovascular Biomedical RChelsea WingRoyal Brompton Campus

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Summary

 

Publications

Citation

BibTex format

@article{Boutsikou:2018:10.1016/j.ijcard.2018.02.082,
author = {Boutsikou, M and Shore, D and Li, W and Rubens, M and Pijuan, A and Gatzoulis, MA and Babu-Narayan, SV},
doi = {10.1016/j.ijcard.2018.02.082},
journal = {International Journal of Cardiology},
pages = {49--53},
title = {Anomalous left coronary artery from the pulmonary artery (ALCAPA) diagnosed in adulthood: varied clinical presentation, therapeutic approach and outcome},
url = {http://dx.doi.org/10.1016/j.ijcard.2018.02.082},
volume = {261},
year = {2018}
}

RIS format (EndNote, RefMan)

TY  - JOUR
AB - IntroductionThe diagnosis of ALCAPA syndrome is sporadic in adulthood, of the limited cases in the literature most are incidental or without symptoms. There is a broad spectrum of clinical manifestations of ALCAPA syndrome however, including sudden cardiac death.CasesWe present herewith a series of 12 consecutive patients with ALCAPA, all diagnosed in adulthood (between 18 and 73years of age). Five patients developed symptoms (breathlessness) after the fourth decade of life, 3 were undiagnosed despite a history of previous mitral valve repair, one presented with heart failure, one with resuscitated cardiac arrest, whereas two patients were asymptomatic. We review in this paper, the clinical history, diagnostic approach and therapeutic choices of ALCAPA syndrome.ConclusionALCAPA syndrome is not confined to childhood, late diagnosis in adulthood has a varied clinical presentation. ALCAPA syndrome should be particularly considered as a potential, albeit uncommon cause of mitral regurgitation and/or dilated cardiomyopathy.
AU - Boutsikou,M
AU - Shore,D
AU - Li,W
AU - Rubens,M
AU - Pijuan,A
AU - Gatzoulis,MA
AU - Babu-Narayan,SV
DO - 10.1016/j.ijcard.2018.02.082
EP - 53
PY - 2018///
SN - 0167-5273
SP - 49
TI - Anomalous left coronary artery from the pulmonary artery (ALCAPA) diagnosed in adulthood: varied clinical presentation, therapeutic approach and outcome
T2 - International Journal of Cardiology
UR - http://dx.doi.org/10.1016/j.ijcard.2018.02.082
UR - http://gateway.webofknowledge.com/gateway/Gateway.cgi?GWVersion=2&SrcApp=PARTNER_APP&SrcAuth=LinksAMR&KeyUT=WOS:000430081000014&DestLinkType=FullRecord&DestApp=ALL_WOS&UsrCustomerID=1ba7043ffcc86c417c072aa74d649202
UR - http://hdl.handle.net/10044/1/61539
VL - 261
ER -